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Paper Title
Desmosomal protein degradation as an underlying cause of arrhythmogenic cardiomyopathy.
PubMed
Paper Journal Title
Sci Transl Med
Paper Citation Count
8
Paper Publication Year
2023
Bio Mention
ACM, Arrhythmogenic cardiomyopathy, Desmosomal protein degradation, PKP2, UPS, adherens, area composita proteins, arrhythmogenic cardiomyopathy, calcium, cardiac dysfunction, desmosomal, desmosomal genes, desmosomal proteins, fibrosis, human, human-induced pluripotent stem cell-derived cardiomyocytes, inherited progressive cardiac disease, isolated cardiomyocytes, lysine, mice, patients, plakophilin-2, ubiquitin
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Author Name
Affiliation
Manuel Mayr
King's College, University of London
Jeroen A A Demmers
Erasmus Medical Center Rotterdam
Christine L Mummery
University Medical Center
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