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Paper Title
Mice lacking dystrophin or alpha sarcoglycan spontaneously develop embryonal rhabdomyosarcoma with cancer-associated p53 mutations and alternatively spliced or mutant Mdm2 transcripts.
PubMed
Paper Journal Title
Am J Pathol
Paper Citation Count
45
Paper Publication Year
2010
Bio Mention
Fkhr, Mdm2, Mdm2 transcripts, Mice, Pax3, Pax3:Fkhr or Pax7:Fkhr translocation mRNA products, Pax7, RMS, Sgca, Sgca(-/-), alpha dystroglycan, alpha sarcoglycan, alveolar, alveolar RMS, alveolar RMS subtypes, cancer, cancers, dystrophin, dystrophin-associated glycoprotein complex, embryonal RMS, embryonal rhabdomyosarcoma, human, insulin-like growth factor 2, mdx, mdx RMS, mdx and, mdx and Sgca(-/-) tumors, mice, murine double minute (mdm)2 protein, muscle, muscular dystrophy, mutant Mdm2 transcripts, p53, p53 mutations, p53-binding domain, phosphatase and tensin homolog gene, phosphorylated Akt, retinoblastoma protein, tumor, tumors
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