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Paper Title
Mitochondrial dysfunction and calcium dysregulation in COQ8A-ataxia Purkinje neurons are rescued by CoQ10 treatment.
PubMed
Paper Journal Title
Brain
Paper Citation Count
6
Paper Publication Year
2023
Bio Mention
-, COQ8A, COQ8A gene, COQ8A-ataxia, COQ8A-ataxia Purkinje neurons, COQ8A-depleted Purkinje neurons, CoQ10, Complex IV, Coq8a, Coq8a-/-, Purkinje neuron, Purkinje neurons, ataxia, calcium, cerebellar Purkinje neurons, cerebellar ataxia, coenzyme Q10, dark cell degeneration, mice, mitochondrial dysfunction, neurodegenerative disorder, primary Purkinje neurons
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Bianca Habermann
CNRS, Institut de Biologie du Developpement de Marseille (IBDM), Aix-Marseille University
Bianca Habermann
CNRS, Institut de Biologie du Developpement de Marseille (IBDM), Aix-Marseille University
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