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Paper Details

Mitochondrial dysfunction and calcium dysregulation in COQ8A-ataxia Purkinje neurons are rescued by CoQ10 treatment.
Brain
6
2023
-, COQ8A, COQ8A gene, COQ8A-ataxia, COQ8A-ataxia Purkinje neurons, COQ8A-depleted Purkinje neurons, CoQ10, Complex IV, Coq8a, Coq8a-/-, Purkinje neuron, Purkinje neurons, ataxia, calcium, cerebellar Purkinje neurons, cerebellar ataxia, coenzyme Q10, dark cell degeneration, mice, mitochondrial dysfunction, neurodegenerative disorder, primary Purkinje neurons
Author NameAffiliation
Bianca HabermannCNRS, Institut de Biologie du Developpement de Marseille (IBDM), Aix-Marseille University
Bianca HabermannCNRS, Institut de Biologie du Developpement de Marseille (IBDM), Aix-Marseille University
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