Skip to Main Content

Author Details

Brian S Appleby
Case Western Reserve University
2005
107
27
PMIDPaper TitleJournal TitlePublished Year
36749840A discriminative event-based model for subtype diagnosis of sporadic Creutzfeldt-Jakob disease using brain MRI.Alzheimers Dement2023
37156880A novel subtype of sporadic Creutzfeldt-Jakob disease with PRNP codon 129MM genotype and PrP plaques.Acta Neuropathol2023
36949796Creutzfeldt-Jakob Disease Misdiagnosed as Multiple System Atrophy.Mov Disord Clin Pract2023
37253983Correction: A novel subtype of sporadic Creutzfeldt-Jakob disease with PRNP codon 129MM genotype and PrP plaques.Acta Neuropathol2023
37180971Feasibility and acceptability of remote smartphone cognitive testing in frontotemporal dementia research.Alzheimers Dement (Amst)2023
36977552Plasma inflammation for predicting phenotypic conversion and clinical progression of autosomal dominant frontotemporal lobar degeneration.J Neurol Neurosurg Psychiatry2023
37431188Network Connectivity Alterations across the MAPT Mutation Clinical Spectrum.Ann Neurol2023
36591730Multisite ALLFTD study modeling progressive empathy loss from the earliest stages of behavioral variant frontotemporal dementia.Alzheimers Dement2023
35262719Prevalence of Surgical Procedures at Symptomatic Onset of Prion Disease.JAMA Netw Open2022
35614914Atypical Case of VV1 Creutzfeldt-Jakob Disease Subtype: Case Report.Front Neurol2022
35584922Sensitivity of the Social Behavior Observer Checklist to Early Symptoms of Patients With Frontotemporal Dementia.Neurology2022
35349636Proposed research criteria for prodromal behavioural variant frontotemporal dementia.Brain2022
35790423Differences in Motor Features of <i>C9orf72</i>, <i>MAPT</i>, or <i>GRN</i> Variant Carriers With Familial Frontotemporal Lobar Degeneration.Neurology2022
36277922Genetic aspects of human prion diseases.Front Neurol2022
34854532The contribution of behavioral features to caregiver burden in FTLD spectrum disorders.Alzheimers Dement2022
35172059Case 5-2022: A 65-Year-Old Woman with Rapidly Progressive Weakness in the Right Arm and Recurrent Falls.N Engl J Med2022
33274461Subtype Diagnosis of Sporadic Creutzfeldt-Jakob Disease with Diffusion Magnetic Resonance Imaging.Ann Neurol2021
33827706Streamlined alpha-synuclein RT-QuIC assay for various biospecimens in Parkinson's disease and dementia with Lewy bodies.Acta Neuropathol Commun2021
33766126Two distinct conformers of PrP<sup>D</sup> type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo.Acta Neuropathol Commun2021
33925126Clinical Use of Improved Diagnostic Testing for Detection of Prion Disease.Viruses2021
33609480Biomarkers and diagnostic guidelines for sporadic Creutzfeldt-Jakob disease.Lancet Neurol2021
33857770Recognition memory and divergent cognitive profiles in prodromal genetic frontotemporal dementia.Cortex2021
34497065Sporadic Creutzfeldt-Jakob Disease in a Very Young Person.Neurology2021
34578375Characterization of Prion Disease Associated with a Two-Octapeptide Repeat Insertion.Viruses2021
34324063Phenotypic diversity of genetic Creutzfeldt-Jakob disease: a histo-molecular-based classification.Acta Neuropathol2021
31272932Individualized atrophy scores predict dementia onset in familial frontotemporal lobar degeneration.Alzheimers Dement2020
32001774Co-existence of PrP<sup>D</sup> types 1 and 2 in sporadic Creutzfeldt-Jakob disease of the VV subgroup: phenotypic and prion protein characteristics.Sci Rep2020
31757870Prion disease incidence in the United States: 2003-2015.Neurology2020
31784375Clinical and volumetric changes with increasing functional impairment in familial frontotemporal lobar degeneration.Alzheimers Dement2020
31953922A case report of genetic prion disease with two different PRNP variants.Mol Genet Genomic Med2020
31914230Assessment of executive function declines in presymptomatic and mildly symptomatic familial frontotemporal dementia: NIH-EXAMINER as a potential clinical trial endpoint.Alzheimers Dement2020
31914218Utility of the global CDR[®] plus NACC FTLD rating and development of scoring rules: Data from the ARTFL/LEFFTDS Consortium.Alzheimers Dement2020
31914217Genetic screening of a large series of North American sporadic and familial frontotemporal dementia cases.Alzheimers Dement2020
33064135Human Prion Disease Surveillance in Washington State, 2006-2017.JAMA Netw Open2020
32571851Diagnosis of prion diseases by RT-QuIC results in improved surveillance.Neurology2020
32733203Case Report: Histopathology and Prion Protein Molecular Properties in Inherited Prion Disease With a <i>De Novo</i> Seven-Octapeptide Repeat Insertion.Front Cell Neurosci2020
32949544Identification of novel risk loci and causal insights for sporadic Creutzfeldt-Jakob disease: a genome-wide association study.Lancet Neurol2020
32478816Evaluation of a New Criterion for Detecting Prion Disease With Diffusion Magnetic Resonance Imaging.JAMA Neurol2020
32560672A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease.Acta Neuropathol Commun2020
32535770Prion propagation estimated from brain diffusion MRI is subtype dependent in sporadic Creutzfeldt-Jakob disease.Acta Neuropathol2020
32371446Revised Self-Monitoring Scale: A potential endpoint for frontotemporal dementia clinical trials.Neurology2020
30612334In Vitro Seeding Activity of Glycoform-Deficient Prions from Variably Protease-Sensitive Prionopathy and Familial CJD Associated with PrP<sup>V180I</sup> Mutation.Mol Neurobiol2019
31872042Nonlinear Z-score modeling for improved detection of cognitive abnormality.Alzheimers Dement (Amst)2019
31366689Clinical Laboratory Tests Used To Aid in Diagnosis of Human Prion Disease.J Clin Microbiol2019
31337719Chronic Wasting Disease in Cervids: Implications for Prion Transmission to Humans and Other Animal Species.mBio2019
30861521Feasibility of Remote Assessment of Human Prion Diseases for Research and Surveillance.Dement Geriatr Cogn Disord2019
31008724Human prion diseases.Curr Opin Infect Dis2019
30914754PMCA-replicated PrP<sup>D</sup> in urine of vCJD patients maintains infectivity and strain characteristics of brain PrP<sup>D</sup>: Transmission study.Sci Rep2019
30718499Publisher Correction: Early preclinical detection of prions in the skin of prion-infected animals.Nat Commun2019
30651538Early preclinical detection of prions in the skin of prion-infected animals.Nat Commun2019
  • 1 - 50 of 107

Recommended Authors

Caitlin S Latimer
University of Washington
Career Start Year 2011
Number of shared co-authors 4
Eva C Schulte
Institute of Psychiatric Phenomics and Genomics (IPPG), LMU University Hospital
Career Start Year 2009
Number of shared co-authors 4
Brandy R Matthews
Indiana University School of Medicine
Career Start Year 2003
Number of shared co-authors 18
Wuxing Yuan
Center for Cancer Research, National Cancer Institute
Career Start Year 1998
Number of shared co-authors 5
Victor W Sung
University of Alabama at Birmingham
Career Start Year 1998
Number of shared co-authors 0
Eric McDade
Washington University St. Louis
Career Start Year 1998
Number of shared co-authors 13
Christopher Dirk Keene
University of Washington
Career Start Year 1998
Number of shared co-authors 21
Karen E Anderson
Georgetown University
Career Start Year 1996
Number of shared co-authors 12
Suman Jayadev
University of Washington
Career Start Year 1995
Number of shared co-authors 13
Howard H Feldman
University of California San Diego
Career Start Year 1995
Number of shared co-authors 24
Huw R Morris
Queen Square Institute of Neurology, University College London
Career Start Year 1991
Number of shared co-authors 19
Gregory A Jicha
University of Kentucky
Career Start Year 1991
Number of shared co-authors 26
Pudugramam Murali Doraiswamy
Duke University School of Medicine
Career Start Year 1990
Number of shared co-authors 15
Stephen Salloway
Butler Hospital, and Warren Alpert Medical School of Brown University
Career Start Year 1988
Number of shared co-authors 21
Paul E Schulz
The University of Texas Health Science Center at Houston, McGovern Medical School
Career Start Year 1988
Number of shared co-authors 3
Nigel J Cairns
Washington University School of Medicine
Career Start Year 1988
Number of shared co-authors 25
Marwan N Sabbagh
Barrow Neurological Institute
Career Start Year 1988
Number of shared co-authors 22
Lefkos T Middleton
Ageing Epidemiology Research Unit, School of Public Health, Imperial College London
Career Start Year 1988
Number of shared co-authors 6
James D Bowen
Swedish Neuroscience Institute
Career Start Year 1987
Number of shared co-authors 15
Simon Lovestone
Janssen Medical Ltd
Career Start Year 1986
Number of shared co-authors 22
Douglas W Scharre
Ohio State University
Career Start Year 1986
Number of shared co-authors 13
Christine M Hulette
Duke University
Career Start Year 1985
Number of shared co-authors 17
Matthew P Frosch
Massachusetts General Hospital and Harvard Medical School
Career Start Year 1984
Number of shared co-authors 21
David B Clifford
Washington University School of Medicine
Career Start Year 1982
Number of shared co-authors 3
Raymond S Turner
Georgetown University
Career Start Year 1981
Number of shared co-authors 15
Lawrence S Honig
University of California
Career Start Year 1975
Number of shared co-authors 26
David J Burn
Population Health Sciences Institute, Newcastle University
Career Start Year 1975
Number of shared co-authors 11
Joseph J Locascio
Harvard Medical School, Massachusetts General Hospital
Career Start Year 1975
Number of shared co-authors 3
Daniel P Perl
Uniformed Services University School of Medicine
Career Start Year 1968
Number of shared co-authors 15
Thomas D Bird
University of Washington School of Medicine
Career Start Year 1965
Number of shared co-authors 19

Collaborators

Mark L Cohen
Co-authored papers 21
Bradley F Boeve
Mayo Clinic Rochester
Co-authored papers 16
Adam L Boxer
UCSF Weill Institute for Neurosciences, University of California san francisco
Co-authored papers 16
Howard J Rosen
UCSF Weill Institute for Neurosciences, University of California san francisco
Co-authored papers 16
Neill R Graff-Radford
Mayo Clinic Florida
Co-authored papers 14
John Kornak
University of California san francisco
Co-authored papers 14
Chiadi U Onyike
Johns Hopkins University School of Medicine
Co-authored papers 14
David S Knopman
Mayo Clinic Rochester
Co-authored papers 10
Bruce L Miller
UCSF Weill Institute for Neurosciences, University of California san francisco
Co-authored papers 10
Ging-Yuek R Hsiung
University of British Columbia
Co-authored papers 10
Joel H Kramer
UCSF Weill Institute for Neurosciences, University of California san francisco
Co-authored papers 9
Arthur W Toga
Keio University School of Medicine
Co-authored papers 8
Jonathan Graff-Radford
Mayo Clinic Rochester
Co-authored papers 8
Rosa Rademakers
University of Antwerp
Co-authored papers 8
Giovanni Coppola
David Geffen School of Medicine, University of California los angeles
Co-authored papers 7
Tatiana Foroud
Indiana University School of Medicine
Co-authored papers 7
Diana R Kerwin
Kerwin Research Center and Memory Care Dallas Texas USA.
Co-authored papers 7
Leonard Petrucelli
Co-authored papers 6
Peter V Rabins
Johns Hopkins School of Medicine
Co-authored papers 6
John Q Trojanowski
University of Pennsylvania
Co-authored papers 6
Anna Karydas
Weill Institute for Neurosciences, University of California san francisco
Co-authored papers 6
Leslie M Shaw
Perelman School of Medicine, University of Pennsylvania
Co-authored papers 6
Alan J Lerner
Case Western Reserve University
Co-authored papers 5
Daniel D Rhoads
Cleveland Clinic Lerner College of Medicine, Case Western Reserve University
Co-authored papers 5
Katrina L Devick
Mayo Clinic Arizona
Co-authored papers 3
James B Leverenz
Lou Ruvo Center for Brain Health, Cleveland Clinic
Co-authored papers 2
Douglas Galasko
Co-authored papers 2
Daniel H Geschwind
University of California los angeles
Co-authored papers 2
Jason Brandt
The Johns Hopkins University School of Medicine
Co-authored papers 1
David M Blass
Johns Hopkins University School of Medicine Abarbanel Mental Health Centre
Co-authored papers 1
Release 1.2