Author details

Full Name

Suh Young Jeong

Affiliation

ORCID

Career Start Year

2002

Papers

H Index

Expertise

CM4AI Collaborator

PMID	Paper Title	Journal Title	Published Year
37745522	Cardiac glycosides restore autophagy flux in an iPSC-derived neuronal model of WDR45 deficiency.		2023
34569265	Dysregulation of Iron Homeostasis in the Central Nervous System and the Role of Ferroptosis in Neurodegenerative Disorders.	Antioxidants and Redox Signaling	2022
36240582	PKAN pathogenesis and treatment.	Molecular Genetics and Metabolism	2022
33150406	KMT2B-related disorders: expansion of the phenotypic spectrum and long-term efficacy of deep brain stimulation.	Brain	2020
31087512	Autosomal dominant mitochondrial membrane protein-associated neurodegeneration (MPAN).	Molecular genetics & genomic medicine	2019
31660701	4'-Phosphopantetheine corrects CoA, iron, and dopamine metabolic defects in mammalian models of PKAN.	EMBO Molecular Medicine	2019
28900161	Acetyl-4'-phosphopantetheine is stable in serum and prevents phenotypes induced by pantothenate kinase deficiency.	Scientific Reports	2017
26547561	Pallidal neuronal apolipoprotein E in pantothenate kinase-associated neurodegeneration recapitulates ischemic injury to the globus pallidus.	Molecular Genetics and Metabolism	2015
23943793	Elevated FGF21 secretion, PGC-1Î± and ketogenic enzyme expression are hallmarks of iron-sulfur cluster depletion in human skeletal muscle.	Hum Mol Genet	2014
23395173	Deletion of iron regulatory protein 1 causes polycythemia and pulmonary hypertension in mice through translational derepression of HIF2Î±.		2013
23035118	Tissue specificity of a human mitochondrial disease: differentiation-enhanced mis-splicing of the Fe-S scaffold gene ISCU renders patient cells more sensitive to oxidative stress in ISCU myopathy.	Journal of Biological Chemistry	2012
22529995	Iron accumulation in deep cortical layers accounts for MRI signal abnormalities in ALS: correlating 7 tesla MRI and pathology.	PLoS One	2012
23351752	Primary cilia utilize glycoprotein-dependent adhesion mechanisms to stabilize long-lasting cilia-cilia contacts.	Cilia	2012
21907923	The glycolytic shift in fumarate-hydratase-deficient kidney cancer lowers AMPK levels, increases anabolic propensities and lowers cellular iron levels.	Cancer Cell	2011
22003390	Iron insufficiency compromises motor neurons and their mitochondrial function in Irp2-null mice.	PLoS ONE	2011
20364084	Glutaredoxin 5 deficiency causes sideroblastic anemia by specifically impairing heme biosynthesis and depleting cytosolic iron in human erythroblasts.	Journal of Clinical Investigation	2010
19851851	Brain iron homeostasis, the choroid plexus, and localization of iron transport proteins.	Metabolic Brain Disease	2009
19158288	Dysregulation of iron homeostasis in the CNS contributes to disease progression in a mouse model of amyotrophic lateral sclerosis.	Journal of Neuroscience	2009
18205174	The protective effects of 15-deoxy-delta-(12,14)-prostaglandin J2 in spinal cord injury.	GLIA	2008
19036966	Ceruloplasmin protects injured spinal cord from iron-mediated oxidative damage.	Journal of Neuroscience	2008
17096403	T cells contribute to lysophosphatidylcholine-induced macrophage activation and demyelination in the CNS.	GLIA	2007
17541408	Ferroxidase activity is required for the stability of cell surface ferroportin in cells expressing GPI-ceruloplasmin.	EMBO Journal	2007
16988052	Age-related changes in iron homeostasis and cell death in the cerebellum of ceruloplasmin-deficient mice.	Journal of Neuroscience	2006
12743117	Glycosylphosphatidylinositol-anchored ceruloplasmin is required for iron efflux from cells in the central nervous system.	Journal of Biological Chemistry	2003
12812757	Immunization with myelin or recombinant Nogo-66/MAG in alum promotes axon regeneration and sprouting after corticospinal tract lesions in the spinal cord.	Molecular and Cellular Neurosciences	2003
12555201	Expression of a membrane-bound form of the ferroxidase ceruloplasmin by leptomeningeal cells.	GLIA	2003
12151537	Ceruloplasmin regulates iron levels in the CNS and prevents free radical injury.	Journal of Neuroscience	2002